Cori’s disease, is an autosomal recessive metabolic disorder that is characterized by defects in the glycogen debranching enzyme amylo-1,6-glucosidase,4-α-glucanotransferase (AGL). It primarily effects the Liver, heart and skeletal muscle. Symptoms can include hyperlipidemia, ketoacidosis, and hypoglycemia. The possible dietary recommendations are as follows: 1. A high protein diet to facilitate gluconeogenesis 2. A ketogenic diet to provide an alternate source of energy 3. Small frequent meals to prevent hypoglycemia 4. A high fat diet Which dietary recommendations can be used to treat this disorder? a) 2 and 4 b) 1 and 2 c) 2 and 3 d) 1 and 3 e) None of the above recommendations would be effective f) 3 and 4 g) 1 and 4

Cori’s disease, is an autosomal recessive metabolic disorder that is characterized by defects in the glycogen debranching enzyme amylo-1,6-glucosidase,4-α-glucanotransferase (AGL). It primarily effects the Liver, heart and skeletal muscle. Symptoms can include hyperlipidemia, ketoacidosis, and hypoglycemia. The possible dietary recommendations are as follows: 1. A high protein diet to facilitate gluconeogenesis 2. A ketogenic diet to provide an alternate source of energy 3. Small frequent meals to prevent hypoglycemia 4. A high fat diet Which dietary recommendations can be used to treat this disorder? a) 2 and 4 b) 1 and 2 c) 2 and 3 d) 1 and 3 e) None of the above recommendations would be effective f) 3 and 4 g) 1 and 4

Nutrition Through The Life Cycle

7th Edition

ISBN:9781337919333

Author:Brown, Judith E.

Publisher:Brown, Judith E.

Chapter17: Adult Nutrition -conditions And Interventions

Section: Chapter Questions

Problem 3RQ

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